Bilateral corneal perforation and iris prolapse as a complication non-peripheral ulcerative keratitis in a patient with fulminant Granulomatosis with Polyangiitis. A case Report. Academic Article

journal

  • Ocular Immunology and Inflammation

abstract

  • Propósito: Reportar un caso de granulomatosis con poliangitis (GPA) con un fulminantefenotipo caracterizado por diversas manifestaciones oculares y sistémicas.Métodos: Informe de caso y comparación de literatura.Resultados: reportamos el caso de un paciente masculino de 58 años con diagnóstico de GPA, que presentó manifestaciones oculares atípicas concomitantes con compromiso sistémico que condujeron a progresión severa y fulminante de la enfermedad.Conclusión: se requiere un diagnóstico precoz y un abordaje interdisciplinario apropiado en pacientes con manifestaciones atípicas de GPA debido a su potencial amenaza a la vida
  • Purpose: To report a case of Granulomatosis with Polyangiitis (GPA) with a fulminantphenotype characterized by diverse ocular and systemic manifestations.Methods: Case report and literature comparison.Results: we report the case of a 58 years old male patient with diagnosis of GPA, who presented with atypical ocular manifestations concomitant with systemic compromise thath led to severe and fulminant progression of the disease.Conclusion: early diagnosis and an appropriate interdisciplinary approach are required in patiens with atypical manifestations of GPA dut t its life-threatening potential

publication date

  • 2020-1-10

edition

  • 10

keywords

  • Corneal Perforation
  • Corneal Ulcer
  • Disease Progression
  • Early Diagnosis
  • Eye Manifestations
  • Granulomatosis with Polyangiitis
  • Iris
  • Prolapse

International Standard Serial Number (ISSN)

  • 0927-3948

number of pages

  • 17

start page

  • 3

end page

  • 20